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  • 1 SMS Medical College Department of Gastroenterology Jaipur Rajasthan India
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Autosomal dominant polycystic liver disease (PCLD) is a systemic hereditary disorder associated with cyst formation in the ductal organs like kidney and liver. Portal hypertension as a presenting manifestation is very rare. We report a case of 58-year-old male with PCLD presenting with portal hypertension and impaired hepatocellular function, managed conservatively.

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