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  • 1 Országos Reumatológiai és Fizioterápiás Intézet Budapest Frankel Leó út 38–40. 1023
  • 2 Semmelweis Egyetem, Általános Orvostudományi Kar III. Belklinika, II. Reumatológiai Tanszéki Csoport (ORFI) Budapest
  • 3 Semmelweis Egyetem, Általános Orvostudományi Kar Szemészeti Klinika Budapest Tömő u. 25–29. 1083

A Behcet-kór multiszisztémás autoimmun betegség változatos klinikai megjelenési tünetekkel. Hazánkban a Behcet-kór a ritka betegségek közé tartozik, a témával foglalkozó közlemények száma elenyésző. Történelmünk során a népcsoportok keveredése, valamint a világszerte növekvő prevalencia és a szerzők tapasztalata is arra utal, hogy a betegség előfordulására az eddig vártnál nagyobb gyakorisággal kell számítani. A szerzők felhívják a figyelmet erre a sokoldalúan megjelenő, sok szakterületet érintő betegségre. A diagnózis nagy kihívást jelent a klinikus számára, akinek tisztában kell lennie a lehetséges tünetek spektrumával és kombinációival. Irodalmi adatok és saját tapasztalataik alapján a szerzők összefoglalják a betegség eddig ismert patogenetikai és patomechanikai tényezőit és a diagnózishoz nélkülözhetetlen szimptómák rendszerét, a kezelés lehetőségeit. A közleménnyel a szerzők a diagnosztikát, a magyar betegpopuláció feltérképezését és jobb kezelését szeretnék segíteni, és kezdeményezik hazai Behcet-regiszter felállítását. Orv. Hetil., 2013, 154, 93–101.

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